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VOLUME 16 , ISSUE 2 ( May-August, 2023 ) > List of Articles

CASE REPORT

Rapunzel Syndrome Presenting with Intussusception and Pancreatitis: A Case Report

Harish V Sutrave, Annapoorni Valliappan, Sivasankar Jayakumar

Keywords : Case report, Children, Ileoileal intussusception, Laparoscopy, Pancreatitis, Rapunzel syndrome, Trichobezoar

Citation Information : Sutrave HV, Valliappan A, Jayakumar S. Rapunzel Syndrome Presenting with Intussusception and Pancreatitis: A Case Report. World J Lap Surg 2023; 16 (2):105-107.

DOI: 10.5005/jp-journals-10033-1567

License: CC BY-NC 4.0

Published Online: 20-12-2023

Copyright Statement:  Copyright © 2023; The Author(s).


Abstract

Background: Bezoars are ingested foreign materials accumulated most commonly in the stomach as a hard mass. A gastric bezoar composed of hair (Trichobezoar) that has a long tail that extends beyond the pylorus throughout the small bowel and very rarely to the cecum is described as Rapunzel syndrome. Case presentation: A 14-year-old girl presented with abdominal pain (4 days) with bilious vomiting (1 day). Contrast-enhanced computed tomography (CECT) scan showed a bezoar extending from the stomach to the small bowel within a jejunojejunal intussusception. Serum amylase levels were also elevated. The entire bezoar was extracted laparoscopically after reducing the jejunojejunal intussusception, subsequently, the patient recovered well and has been well after 2 years. Conclusion: Patients with Rapunzel syndrome can present with intussusception or with pancreatitis, or rarely with both, as seen in our patient.

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